Neuromyelitis optica is characterised by optic neuritis, longitudinallyextensive transverse myelitis and presence of antiaquaporin4 antibodies in the serum. Les symptomes moteurs et urinaires sont souvent au second plan. In about 20% of cases, the etiology remains unknown even after a longterm followup. Les myelopathies inflammatoires aigues, aussi appelees myelites aigues ma, constituent.
The discovery of a novel serum autoantibody termed nmoigg or aqp4ab in a subset of patients in 2004 has revived interest in neuromyelitis optica nmo. Acute transverse myelitis is defined as an acquired neuro immune disorder of the spinal cord, which occurs as a consequence of a primary event, or. Nichttraumatische akute querschnittsyndrome hess related information. Epidemiology of neuromyelitis optica in latin america mp. The prognosis of acute and subacute transverse myelopathy. Presentations cliniques trois tableaux cliniques medullaires sont observables. An approach to the diagnosis of acute transverse myelitis anu jacob, m. Cliniquement,lespatientspresententunsyndrome lesionnel, souslesionnel et rachidien, ce dernier etant souvent absent.
Transverse myelitis tm is a rare neurological condition in which the spinal cord is inflamed. Proposal for diagnostic criteria of tropical spastic. Gaze palsy, hypogeusia and a probable association with. To analyze the magnetic resonance mr imaging findings in idiopathic acute transverse myelitis iatm in relation to pathologic findings and mr findings in guillainbarre syndrome and ischemia. Acute transverse myelitis is defined as an acquired neuro immune disorder of the spinal cord, which occurs as a consequence of a primary event, or directly related to an autoimmune inflammatory. Myelite aigue transverse evolution garcon, 14 ans, paraplegie flasque, bonne recuperation a 8 mois epu trousseau 2008 fille, 10 ans, paraplegie flasque subaigue, 10 mois plus tard. The history of neuromyelitis optica pubmed central pmc.
Nichttraumatische akute querschnittsyndrome praxis. Myelopathie aigue, myelite, myelite partielle, myelite transverse, myelite infectieuse, sclerose. The full text of this article is available in pdf format. Semiautomatic quantification of spinal cord atrophy from 3dimensional mr images. The spectrum of neuromyelitis optica the lancet neurology. However, nonopticospinal central nervous system manifestations have been increasingly recognised. Myelite transverse aigue troubles neurologiques edition. Awareness of the widening clinical spectrum of neuromyelitis optica unified within the. Please use one of the following formats to cite this article in your essay, paper or report. Spinal cord involvement in nmosd typically presents with transverse myelitis, characterized by symmetric paraparesis or quadriparesis, bladder dysfunction, and sensory loss below the level of the spinal cord lesion.
Complexity and heterogeneity in demyelinating disease. Jan 15, 20 the discovery of a novel serum autoantibody termed nmoigg or aqp4ab in a subset of patients in 2004 has revived interest in neuromyelitis optica nmo. Complexity and heterogeneity in demyelinating disease brain. By continuing to use our website, you are agreeing to our use of cookies. Myelite aigue transverse et primoinfection a epsteinbarr virus article in madecine et maladies infectieuses 422 february 2012 with 24 reads how we measure reads. We have given names to diseases according to the clinical phenomena exhibited, according to etiologic factors and according to anatomic localization or changes. Review open access the history of neuromyelitis optica.
Herpes simplex virus2 myelitis persistence of viral. Myelite aigue transverse et primoinfection a epsteinbarr. Acute transverse myelopathy atm is a large group from various etiologies including multiple sclerosis, systemic diseases, postinfectious myelopathy, spinal cord infarct and neuromyelitis optica. Vascular malformations of the spinal cord archives. This is a report of nine patients who were treated between 1993 and 1996. Refractory longitudinally extensive transverse myelitis. Neurologie 17071a10 myelopathies aigues em consulte.
Transverse implies that the inflammation extends horizontally across the spinal cord. Nineteen had symptoms of a recent acute infectious illness, 3 had cancer, and 1 had undergone a recent operation. The title of this paper might be altered, have additional descriptive terms appended, or even shortened. Transverse myelitis wikimili, the best wikipedia reader. Refractory longitudinally extensive transverse myelitis responsive to cyclophosphamide volume 44 issue 6 laura j. Acute transverse myelitis atm is a rare disease in childhood and adolescence. An approach to the diagnosis of acute transverse myelitis. Time is of the essence when it comes to rare neuroimmune disorders and the time to get awareness out is now. Caracteristique dune myelite longitudinale etendue. Neuromyelitis optica spectrum disorder and antimog. These nine cases, in five of which the lesions were.
Elisa is one of srnas hope ambassadors, a community of heroes for a common cause. Neuromyelitis optica has a worldwide distribution, poor prognosis, and has long been thought of as a variant of multiple sclerosis. There is some evidence that the term neuromyelite was chosen by devic and gault in analogy with neurocerebrite, a term associated with the name of august pierret. While the history of classical multiple sclerosis has been extensively studied, only little is known about the history of nmo. Partial transverse myelitis and partial myelitis are terms sometimes used to specify inflammation that only affects part of the width of the spinal cord. The fact that the congress proceedings with devics abstract appeared only in 1895, i.
16 635 683 884 392 637 1106 1453 1517 726 474 494 1375 1435 347 405 114 384 850 1645 786 1276 1576 1157 1440 294 1145 1168 683 139 977 1235 215 1314 804 1513 1167 838 1091 768 136 471 599 27 1014 783 146 870 235 383 197